282 Chapter 9 Supplementary Table 1: Continued. Variable name Definition NT1 (n=752) NT2 (n=200) IH (n=126) Normalized outcome options n Median (IQR) / Percentage n Median (IQR) / Percentage n Median (IQR) / Percentage Hypocretin level Hypocretin-1 level as measured in cerebrospinal fluid 236 12.0 (0.0-55.0) 29 228.0 (143.5337.0) 46 302.5 (253.0368.0) 0-1 = 0-382 pg / mL HLA – DQB1*0602 HLA – DQB1*0602 positivity 552 93.8% 100 53.0% 58 43.1% 0 = No, 1 = Yes HLA – DQA1*0102 HLA – DQA1*0102 positivity 185 74.6% 34 50.0% 2 0.0% 0 = No, 1 = Yes Age onset EDS Age onset cataplexy Age onset disturbed NS Age at onset of excessive daytime sleepiness, cataplexy or disturbed nocturnal sleep 736 709 469 19.8 (14.529.5) 23.3 (16.333.0) 23.8 (16.134.8) 197 5 68 19.3 (14.828.3) 23.8 (9.4-37.4) 24.0 (17.034.7) 123 4 24 18.3 (14.8-26.5) 20.4 (9.4-30.4) 26.7 (15.1-37.8) Age EDS: 0-1 = 3.6-56.1 years Age cataplexy: 0-1 = 5.9-60.7 years Age disturbed NS: 0-1 = 6.660.9 years
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