CHAPTER 10 254 assessment, which is developed to assess the occupational performance in people of any age, gender, culture or disability with information-processing difficulties. The two-stage assessment observes meaningful activities with the performance of a behavioural task analysis in Stage One, resulting in a personal level of occupational performance mastery, and a cognitive task analysis in Stage Two, resulting in a efficiency score on the application of cognitive strategies required for successful task performance. The assessment can be administered based on live observations or video-material.10-12 There are 16 studies known by the authors, that focused on establishing the PRPP-Assessment’s psychometric properties, including its face validity13-16, construct validity17-22, criterion validity23, 24, inter-rater reliability16, 25-28 and intra-rater reliability26. In addition, clinical utility was evaluated in three studies22, 29, 30 and in ten studies14, 31-39 the PRPP-Assessment was used in longitudinal designs, even in some cases as outcome measure, adding to the body of knowledge on the responsiveness of the assessment. However, most of these studies focus on homogenic groups and not on heterogenic groups of children with multiple disabilities. Although the PRPP-Assessment has potential to serve as a personalized occupation-based assessment for children with a mitochondrial disorder, the psychometric properties for this target group are yet unknown. This is wat we aimed to assess in this thesis. The heterogenic group of children with mitochondrial disorder could serve as an example for the common group of children in OT- practice; if we can measure this target group, the PRPP-Assessment can be applied to many other target groups! The chapter concludes with an outline of this thesis. In our studies we first focused on uncovering the perspective of the child and ways to do that and next, we focused on the implementation and psychometric properties of the PRPP-Assessment. Chapter 2 – Daily activities of children with mitochondrial disorder as noted in charts The second chapter in this thesis describes the retrospective chart study aimed to explore the activities reported in patient records of children with a genetically confirmed mitochondrial disorder. Seventeen patient records of children with mitochondrial disorder (age 4 – 18 years) were reviewed on reported activities by (allied) health care professionals (as part of their professional reasoning obligations) and analysed with directed content analysis. In order to get a grip on the overview and the target group, we suggested to stratify the heterogenic group of children into three functional profiles based on their functional capacities (cognitivedevelopmental level, grossmotor development, ambulation and speech abilities). The three functional profiles were: global low functioning, low cognitive functioning with a moderate to normal ambulation and global moderate functioning.
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